{"id":764,"date":"2023-01-12T06:03:14","date_gmt":"2023-01-12T06:03:14","guid":{"rendered":"https:\/\/pkudsehcp-dev-001.azurewebsites.net\/es-us\/?page_id=764"},"modified":"2024-09-16T13:00:05","modified_gmt":"2024-09-16T13:00:05","slug":"opciones-de-tratamiento-de-la-pku","status":"publish","type":"page","link":"https:\/\/hcp.biomarin.com\/es-la\/pku\/opciones-de-tratamiento-de-la-pku\/","title":{"rendered":"Opciones de manejo de PKU"},"content":{"rendered":"<div id=\"acf-block-63f65094b7d2f\" class=\"hero hero-no-overlay\">\n            <div class=\"hero-background-image hero-background-image-desktop\" style=\"background-image: url(https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-content\/uploads\/sites\/6\/2023\/01\/PKU_Tree_DSE_Website_Interior_2022_v1_RGB_FIN.jpg?v=0.90);\"><\/div>\n\t    <div class=\"hero-background-image hero-background-image-mobile\" style=\"background-image: url(https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-content\/uploads\/sites\/6\/2023\/01\/PKU_Tree_DSE_Website_Interior_2022_v1_RGB_FIN.jpg?v=0.90);\"><\/div>\n    \t<div class=\"overlay\"><\/div>\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t\t<div class=\"hero-content\">\n\t\t\t    \t\t\t\t\t\t\t\t\t\t\t\t    <h1>El control de fenilcetonuria es para toda la vida<sup>1<\/sup>\n<\/h1>\n\t\t\t\t\t\t\t\t\t\t\t\t\n                <p class=\"inline-buttons\">\n                                                        <\/p>\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n<div id=\"acf-block-63f65094b7d96\" class=\"block wrapped-content bg-band block-zero-top block-zero-bottom\">\n    <div class=\"wrapper\">\n        <div class=\"inner-wrapper\">\n                \n<div id=\"acf-block-63f65094b7db4\" class=\"block-wysiwyg\">\n            <h2 style=\"text-align: left\">\u00bfCu\u00e1les son las opciones para los pacientes con PKU?<\/h2>\n<p>En combinaci\u00f3n con una dieta con restricci\u00f3n de fenilalanina (Phe), existen opciones farmacol\u00f3gicas que pueden ayudar a reducir los niveles de Phe en sangre de pacientes con PKU.<\/p>\n<h3>Terapia diet\u00e9tica<\/h3>\n<p>Globalmente, el abordaje para el control de fenilcetonuria (PKU) ha sido una dieta altamente restringida en fenilalanina (Phe) y suplementos de terapia nutricional medicamentosa<sup>1-3<\/sup><\/p>\n    <\/div>\n        <\/div>\n    <\/div>\n<\/div>\n\n<div id=\"acf-block-63f65094b7dd1\" class=\"block cards cards-3-col bg-band bg-band-white block-tight-top block-tight-bottom\">\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t\t<div class=\"cards-title\">\n\t\t\t    \t\t\t\t\t\t\t<\/div>\n\t\t\t<div class=\"cards-wrapper\">\n\t\t\t    \n<div id=\"acf-block-63f65094b7df0\" class=\"card\" data-muted-autoplay=\"false\">\n    \t    \n\n                    <img decoding=\"async\" class=\"card-image\" src=\"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-content\/uploads\/sites\/6\/2023\/01\/nutrients.svg\" alt=\"Icono de prote\u00edna\" \/>        \n\t    <div class=\"card-content\">\n                            <h4>Necesidades de nutrientes para la deficiencia de la enzima fenilalanina hidroxilasa (PAH)\n<\/h4>\n        \n                                                                                                            <p>Restricci\u00f3n de ingesta natural de prote\u00ednas y sustituci\u00f3n por una prote\u00edna (mezcla de amino\u00e1cidos) desprovista de Phe<sup>1<\/sup><\/p>\n                                                                                    <\/div>\n<\/div>\n\n<div id=\"acf-block-63f65094b7e0c\" class=\"card\" data-muted-autoplay=\"false\">\n    \t    \n\n                    <img decoding=\"async\" class=\"card-image\" src=\"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-content\/uploads\/sites\/6\/2023\/01\/medical_foods.svg\" alt=\"Icono de f\u00f3rmula\" \/>        \n\t    <div class=\"card-content\">\n                            <h4>Alimentos medicinales para deficiencia de PAH\n<\/h4>\n        \n                                                                                                            <p>Los suplementos alimentarios\/f\u00f3rmulas medicinales para PKU proporcionan prote\u00ednas, calor\u00edas y otros nutrientes y ayudan a facilitar el cumplimiento de restricci\u00f3n diet\u00e9tica de Phe<sup>1<\/sup><\/p>\n                                                                                    <\/div>\n<\/div>\n\n<div id=\"acf-block-63f65094b7e21\" class=\"card\" data-muted-autoplay=\"false\">\n    \t    \n\n                    <img decoding=\"async\" class=\"card-image\" src=\"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-content\/uploads\/sites\/6\/2023\/01\/dietry_control.svg\" alt=\"Control diet\u00e9tico con icono de PKU\" \/>        \n\t    <div class=\"card-content\">\n                            <h4>Alimentos modificados con bajo contenido de prote\u00edna<sup>1<\/sup>\n<\/h4>\n        \n                                                                                                            <p>Los alimentos modificados con bajo contenido de prote\u00edna ayudan a saciar a los pacientes<\/p>\n                                                                                    <\/div>\n<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n<div id=\"acf-block-63f65094b7e61\" class=\"block wrapped-content block-zero-bottom\">\n    <div class=\"wrapper\">\n        <div class=\"inner-wrapper\">\n                \n<div id=\"acf-block-63f65094b7e71\" class=\"block-wysiwyg\">\n            <h2>Conozca m\u00e1s sobre PKU<\/h2>\n    <\/div>\n        <\/div>\n    <\/div>\n<\/div>\n\n<div id=\"acf-block-63f65094b7e86\" class=\"block cards cards-2-col block-tight-top block-tight-bottom\">\n\t<div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t\t<div class=\"cards-title\">\n\t\t\t    \t\t\t\t\t\t\t<\/div>\n\t\t\t<div class=\"cards-wrapper\">\n\t\t\t    \n<div id=\"acf-block-63f65094b7ea4\" class=\"card card-product card-fixed-button card-centered\" data-muted-autoplay=\"false\">\n    \t    \n\n                    <img decoding=\"async\" class=\"card-image\" src=\"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-content\/uploads\/sites\/6\/2023\/01\/symptoms_icon.svg\" alt=\"Icono de s\u00edntomas de niveles de Phe no controlados\" \/>        \n\t    <div class=\"card-content\">\n                            <h4>\u00bfUsted conoce los s\u00edntomas cuando la Phe esta descontrolada?\n<\/h4>\n        \n                                                                                                                                                                                                                                                                                    \n                                                                                        <\/div>\n                                <div class=\"card-actions\">\n                            \n                            <p><a class=\"button\" href=\"https:\/\/hcp.biomarin.com\/es-la\/pku\/desafios-de-pku\/\" target=\"_self\">Conozca m\u00e1s<\/a><\/p>\n                                                                                    <\/div>\n<\/div>\n\n<div id=\"acf-block-63f65094b7ec0\" class=\"card card-product card-fixed-button card-centered\" data-muted-autoplay=\"false\">\n    \t    \n\n                    <img decoding=\"async\" class=\"card-image\" src=\"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-content\/uploads\/sites\/6\/2023\/01\/dietry_promo_icon.svg\" alt=\"Control diet\u00e9tico con icono de PKU\" \/>        \n\t    <div class=\"card-content\">\n                            <h4>88% de los pacientes con PKU luchan para mantener el control de Phe en sangre solo con una dieta restricta en Phe<sup>4<\/sup>\n<\/h4>\n        \n                                                                                                                                                                                                                                                                                    \n                                                                                        <\/div>\n                                <div class=\"card-actions\">\n                            \n                            <p><a class=\"button\" href=\"https:\/\/hcp.biomarin.com\/es-la\/pku\/dieta-para-pku\/\" target=\"_self\">Conozca porque<\/a><\/p>\n                                                                                    <\/div>\n<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n<div id=\"Mant\u00e9ngase-actualizado\" class=\"block hcp-sign-up-form\">\n    <div class=\"wrapper\">\n        <div class=\"inner-wrapper\">\n                            <h2>Mant\u00e9ngase actualizado con la informaci\u00f3n m\u00e1s recientes sobre PKU\n<\/h2>\n                        <div class=\"block form-box\">\n                                    <p>Reg\u00edstrese abajo para entrar en contacto con un representante de BioMarin, conozca m\u00e1s sobre los pr\u00f3ximos eventos y noticias sobre PKU o solicitar una conversaci\u00f3n entre pares.<\/p>\n<p><strong>* Campos obligatorios<\/strong><\/p>\n                \n                <form id=\"hcp-sign-up\" name=\"Stay connected with the latest PKU information\">\n                    <div class=\"form-item check-item\">\n                        <input type=\"checkbox\" id=\"connect-local-rep\" name=\"connect_local_rep\">\n                        <label for=\"connect-local-rep\">Con\u00e9ctese con un representante local de BioMarin<\/label>\n                    <\/div>\n\n                    <div class=\"form-item\">\n                        <label for=\"first-name\">Primer nombre<span class=\"required\">*<\/span><\/label>\n                        <input class=\"text\" id=\"first-name\" type=\"text\" required\n                        data-pristine-required-message=\"Ingrese su primer nombre.\">\n                    <\/div>\n\n                    <div class=\"form-item\">\n                        <label for=\"last-name\">Apellido<span class=\"required\">*<\/span><\/label>\n                        <input class=\"text\" id=\"last-name\" type=\"text\" required\n                        data-pristine-required-message=\"Ingrese su apellido.\">\n                    <\/div>\n\n                    <div class=\"form-item\">\n                        <label for=\"medical-speciality\">Especialidad<span class=\"required\">*<\/span><\/label>\n                        <select class=\"text\" id=\"medical-speciality\" required\n                        data-pristine-required-message=\"Seleccione su especialidad m\u00e9dica.\">\n                            <option value=\"\">Por favor, seleccione su especialidad m\u00e9dica<\/option>\n                            <option value=\"Anesthesiology\">Anestesiolog\u00eda<\/option>\n                            <option value=\"Audiology\">Audiolog\u00eda<\/option>\n                            <option value=\"Behavioral Neurology &#038; Neuropsychiatry\">Neurolog\u00eda del Comportamiento y Neuropsiquiatr\u00eda<\/option>\n                            <option value=\"Biology\">Biolog\u00eda<\/option>\n                            <option value=\"Biomedical Engineering\">Ingenier\u00eda Biom\u00e9dica<\/option>\n                            <option value=\"Cardiology\">Cardiolog\u00eda<\/option>\n                            <option value=\"Clinical Biochemical Genetics\">Gen\u00e9tica Bioqu\u00edmica Cl\u00ednica<\/option>\n                            <option value=\"Dentistry and Odontology\">Odontolog\u00eda<\/option>\n                            <option value=\"Dermatology\">Dermatolog\u00eda<\/option>\n                            <option value=\"Diagnostic Radiology\">Radiolog\u00eda diagn\u00f3stica<\/option>\n                            <option value=\"Electoencephalography\">Electroencefalograf\u00eda<\/option>\n                            <option value=\"Endocrinology, Diabetes &#038; Metabolism\">Endocrinolog\u00eda, Diabeter y Metabolismo<\/option>\n                            <option value=\"ENT\/ Otorhinolaryngologist\">Otorrinolaring\u00f3logo<\/option>\n                            <option value=\"Epileptology\">Epileptolog\u00eda<\/option>\n                            <option value=\"Gastroenterology\">Gastroenterolog\u00eda<\/option>\n                            <option value=\"General Practice\/Family\">Cl\u00ednica general\/familiar<\/option>\n                            <option value=\"Genetics\">Gen\u00e9tica<\/option>\n                            <option value=\"Hearing and Speech\">Terapia del lenguaje<\/option>\n                            <option value=\"Hematology\">Hematolog\u00eda<\/option>\n                            <option value=\"Hematology&#038;Oncology\">Hematolog\u00eda y Oncolog\u00eda<\/option>\n                            <option value=\"Hepatology\">Hepatolog\u00eda<\/option>\n                            <option value=\"Infectious Diseases\">Enfermedades infecciosas<\/option>\n                            <option value=\"Intensive Care\">Tratamiento intensivo<\/option>\n                            <option value=\"Internal Medicine\">Medicina Interna<\/option>\n                            <option value=\"Kinesiology\">Kinesiolog\u00eda<\/option>\n                            <option value=\"Laboratory Management\">Gesti\u00f3n de laboratorio<\/option>\n                            <option value=\"Medical Student\">Estudiante de medicina<\/option>\n                            <option value=\"Neonatology\">Neonatolog\u00eda<\/option>\n                            <option value=\"Nephrology\">Nefrolog\u00eda<\/option>\n                            <option value=\"Neurology\">Neurolog\u00eda<\/option>\n                            <option value=\"Neuromuscular Medicine\">Medicina neuromuscular<\/option>\n                            <option value=\"Nutrition, Metabolic\">Nutrici\u00f3n metab\u00f3lica<\/option>\n                            <option value=\"Nutritionist\">Nutricionista<\/option>\n                            <option value=\"Obstetrics\">Obstetricia<\/option>\n                            <option value=\"Occupation Health\">Salud ocupacional<\/option>\n                            <option value=\"Oncology\">Oncolog\u00eda<\/option>\n                            <option value=\"Ophthalmology\">Oftalmolog\u00eda<\/option>\n                            <option value=\"Orthopedics\">Ortoped\u00eda<\/option>\n                            <option value=\"Paliative\/Hospice\">Paliativo<\/option>\n                            <option value=\"Pediatric Allergy\/Immunology\">Alergia\/Inmunolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Anesthesiology\">Anestesiolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Cardiology\">Cardiolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Dentistry\">Odont\u00f3logo pedi\u00e1trico<\/option>\n                            <option value=\"Pediatric Endocrinology\">Endocrinolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Endocrinology, Diabetes &#038; Metabolism\">Endocrinolog\u00eda Pedi\u00e1trica, Diabetes y Metabolismo<\/option>\n                            <option value=\"Pediatric ENT\">Otorrinolaringolog\u00eda pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Gastroenterology\">Gastroenterolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Gastroenterology &#038; Metabolism\">Gastroenterolog\u00eda y metabolismo pedi\u00e1tricos<\/option>\n                            <option value=\"Pediatric Genetics\">Gen\u00e9tica pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Hematology\">Hematolog\u00eda pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Hematology-Oncology\">Hematolog\u00eda-Oncolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Metabolism\">Metabolismo pedi\u00e1trico<\/option>\n                            <option value=\"Pediatric Neurology\">Neurolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Neurosurgery\">Neurocirug\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Oncology\">Oncolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Ophthalmology and Strabismus Specialist\">Especialista en oftalmolog\u00eda pedi\u00e1trica y estrabismo<\/option>\n                            <option value=\"Pediatric Orthopedics\">Ortopedia pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Pneumology\">Neumolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Radiology\">Radiolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatric Rheumatology\">Reumatolog\u00eda Pedi\u00e1trica<\/option>\n                            <option value=\"Pediatrics\">Pediatr\u00eda<\/option>\n                            <option value=\"Phonoaudiology\">Terapia del lenguaje<\/option>\n                            <option value=\"Physiatry\">Fisiatr\u00eda<\/option>\n                            <option value=\"Physician Assistant\">M\u00e9dico asistente<\/option>\n                            <option value=\"Physiotherapy\">Fisioterapia<\/option>\n                            <option value=\"Primary Care\">Atenci\u00f3n primaria<\/option>\n                            <option value=\"Psychology\/Psychiatry\">Psicolog\u00eda\/Psiquiatr\u00eda<\/option>\n                            <option value=\"Pulmonology\">Neumolog\u00eda<\/option>\n                            <option value=\"Radiology (MRI imaging)\">Radiolog\u00eda<\/option>\n                            <option value=\"Research\">Investigador<\/option>\n                            <option value=\"Rheumatology\">Reumatolog\u00eda<\/option>\n                            <option value=\"Surgery\">Cirug\u00eda<\/option>\n                            <option value=\"Traumatology\">Traumatolog\u00eda<\/option>\n                            <option value=\"Other\">Otro<\/option>\n                        <\/select>\n                    <\/div>\n\n                    <div class=\"form-item\">\n                        <label for=\"email\">Direcci\u00f3n de e-mail<span class=\"required\">*<\/span><\/label>\n                        <input class=\"text\" id=\"email\" type=\"email\" required\n                        data-pristine-required-message=\"Ingrese su direcci\u00f3n de e-mail.\"\n                        data-pristine-email-message=\"Este campo requiere una direcci\u00f3n de e-mail v\u00e1lida.\">\n                    <\/div>\n\n                    <div class=\"form-item\">\n                        <label for=\"country\">Pa\u00eds<span class=\"required\">*<\/span><\/label>\n                        <select class=\"text\" id=\"country\" required\n                        data-pristine-required-message=\"Selecciona tu pais.\">\n                            <option value=\"\">Por favor, seleccione su pa\u00eds<\/option>\n                            <option value=\"ARGENTINA\">Argentina<\/option>\n                            <option value=\"BOLIVIA\">Bolivia<\/option>\n                            <option value=\"CHILE\">Chile<\/option>\n                            <option value=\"COLOMBIA\">Colombia<\/option>\n                            <option value=\"COSTA RICA\">Costa Rica<\/option>\n                            <option value=\"ECUADOR\">Ecuador<\/option>\n                            <option value=\"EL SALVADOR\">El Salvador<\/option>\n                            <option value=\"GUATEMALA\">Guatemala<\/option>\n                            <option value=\"MEXICO\">M\u00e9xico<\/option>\n                            <option value=\"NICARAGUA\">Nicar\u00e1gua<\/option>\n                            <option value=\"PANAMA\">Panam\u00e1<\/option>\n                            <option value=\"PARAGUAY\">Paraguay<\/option>\n                            <option value=\"PERU\">Peru<\/option>\n                            <option value=\"URUGUAI\">Uruguai<\/option>\n                            <option value=\"OTHER\">Otro<\/option>\n                        <\/select>\n                    <\/div>\n\n                    <div class=\"form-item check-item\">\n                        <input type=\"checkbox\" id=\"accept-ts-cs\" name=\"accept_ts_cs\" required\n                        data-pristine-required-message=\"Por favor, acepte los t\u00e9rminos de uso.\">\n                        <label for=\"accept-ts-cs\">Al enviar su informaci\u00f3n y confirmar su registro, usted declara, para los debidos efectos legales, que la informaci\u00f3n proporcionada es verdadera, siendo responsable de cualquier inexactitud, falsedad, error y cualesquiera consecuencias que de ello se deriven y aceptando la <a href=\"https:\/\/www.biomarin.com\/data-privacy-center\/\" target=\"_blank\">Pol\u00edtica de Privacidad de BioMarin<\/a> y los <a href=\"https:\/\/medinfoterms.com\/\" target=\"_blank\">T\u00e9rminos de Uso<\/a> y acepta el procesamiento de sus Datos personales seg\u00fan lo establecido en el mismo, incluido que sus Datos personales se almacenar\u00e1n en bases de datos de BioMarin ubicadas, entre otras, en Am\u00e9rica Latina, Europa y\/o Estados Unidos. De acuerdo con la Pol\u00edtica de Privacidad de BioMarin, sus Datos Personales se mantendr\u00e1n seguros, de acuerdo con las leyes y regulaciones aplicables, y podr\u00e1n usarse para (i) invitarlo a participar en programas que BioMarin desarrolla por s\u00ed mismo y\/o junto con sus socios, (ii) realizar actividades relacionadas con el objeto social de BioMarin, (iii) realizar estudios epidemiol\u00f3gicos e investigaciones de resultados, (iv) comunicar informaci\u00f3n sobre enfermedades del portafolio de BioMarin, (v) comunicar informaci\u00f3n sobre los productos de BioMarin a profesionales de la salud a trav\u00e9s de nuestros representantes de ventas o equipo m\u00e9dico, nuestros sitios web, correo electr\u00f3nico, centros de llamadas, correo postal y otros canales, incluidas comunicaciones y otras promociones de marketing, seg\u00fan corresponda, (vi) realizar simposios, conferencias y otros programas educativos y cient\u00edficos, de BioMarin mismo o de terceros; y (vii) realizar estudios de mercado. Si tiene alguna pregunta sobre el procesamiento de sus datos personales o desea ejercer sus derechos, comun\u00edquese con BioMarin a trav\u00e9s del correo electr\u00f3nico <a href=\"mailto:LATAMDataPrivacy@ bmrn.com\">LATAMDataPrivacy@bmrn.com<\/a>.<span class=\"required\">*<\/span><\/label>\n                    <\/div>\n\n                    <div class=\"form-item\">\n                        <input type=\"submit\" class=\"button\" value=\"Enviar\">\n                    <\/div>\n                <\/form>\n                <form id=\"mktoForm_3470\" style=\"display:none;\"><\/form>\n            <\/div>\n\n            <div class=\"block form-success-confirmation\" style=\"display:none;\">\n                                    <h3>\u00a1Muchas gracias!<\/h3>\n<p>En breve nos pondremos en contacto con informaci\u00f3n adicional.<\/p>\n                                            <\/div>\n        <\/div>\n    <\/div>\n<\/div>\n\n<div id=\"acf-block-63f65094b7efc\" class=\"block references\">\n    <div class=\"wrapper\">\n\t\t<div class=\"inner-wrapper\">\n\t\t    \t\t\t    <h4>Referencias:\n<\/h4>\n\t\t\t\t\t\t                <ol>\n                                                                                                                        <li><span>Vockley J, Andersson HC, Antshel KM, et al; American College of Medical Genetics and Genomics Therapeutic Committee. Phenylalanine hydroxylase deficiency: diagnosis and management guidelines. <em>Genet Med.<\/em> 2014;16(2):188-200.\n<\/span><\/li>\n                                                                                                                                                <li><span>van Spronsen FJ, van Wegberg AMJ, Ahring K, et al. Key European guidelines for the diagnosis and management of patients with phenylketonuria.<em> Lancet Diabetes Endocrinol.<\/em> 2017;5(9):743-756.\n<\/span><\/li>\n                                                                                                                                                <li><span>Rocha JC, MacDonald A. Dietary intervention in the management of phenylketonuria: current perspectives. <em>Ped Health Med Ther.<\/em> 2016;7:155-163.\n<\/span><\/li>\n                                                                                                                                                <li><span>Enns GM, Koch R, Brumm V, Blakely E, Suter R, Jurecki E. Suboptimal outcomes in patients with PKU treated early with diet alone: revisiting the evidence. <em>Mol Genet Metab<\/em>. 2010;101(2-3):99-109.\n<\/span><\/li>\n                                                            <\/ol>\n\t\t\t\t\t<\/div>\n\t<\/div>\n<\/div>","protected":false},"excerpt":{"rendered":"","protected":false},"author":3,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"inline_featured_image":false,"footnotes":""},"class_list":["post-764","page","type-page","status-publish","hentry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Opciones de tratamiento y terapia diet\u00e9tica de fenilcetonuria (PKU)<\/title>\n<meta name=\"description\" content=\"En combinaci\u00f3n con una dieta con restricci\u00f3n de fenilalanina (Phe), existen otras opciones que pueden ayudar a reducir los niveles de Phe en sangre de pacientes con PKU.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/hcp.biomarin.com\/es-la\/pku\/opciones-de-tratamiento-de-la-pku\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Opciones de tratamiento y terapia diet\u00e9tica de fenilcetonuria (PKU)\" \/>\n<meta property=\"og:description\" content=\"En combinaci\u00f3n con una dieta con restricci\u00f3n de fenilalanina (Phe), existen otras opciones que pueden ayudar a reducir los niveles de Phe en sangre de pacientes con PKU.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/hcp.biomarin.com\/es-la\/pku\/opciones-de-tratamiento-de-la-pku\/\" \/>\n<meta property=\"og:site_name\" content=\"BioMarin PKU DSE HCP ES-LA\" \/>\n<meta property=\"article:modified_time\" content=\"2024-09-16T13:00:05+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/hcp.biomarin.com\\\/es-la\\\/pku\\\/opciones-de-tratamiento-de-la-pku\\\/\",\"url\":\"https:\\\/\\\/hcp.biomarin.com\\\/es-la\\\/pku\\\/opciones-de-tratamiento-de-la-pku\\\/\",\"name\":\"Opciones de tratamiento y terapia diet\u00e9tica de fenilcetonuria (PKU)\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/hcp.biomarin.com\\\/es-la\\\/pku\\\/#website\"},\"datePublished\":\"2023-01-12T06:03:14+00:00\",\"dateModified\":\"2024-09-16T13:00:05+00:00\",\"description\":\"En combinaci\u00f3n con una dieta con restricci\u00f3n de fenilalanina (Phe), existen otras opciones que pueden ayudar a reducir los niveles de Phe en sangre de pacientes con PKU.\",\"breadcrumb\":{\"@id\":\"https:\\\/\\\/hcp.biomarin.com\\\/es-la\\\/pku\\\/opciones-de-tratamiento-de-la-pku\\\/#breadcrumb\"},\"inLanguage\":\"es\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\\\/\\\/hcp.biomarin.com\\\/es-la\\\/pku\\\/opciones-de-tratamiento-de-la-pku\\\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\\\/\\\/hcp.biomarin.com\\\/es-la\\\/pku\\\/opciones-de-tratamiento-de-la-pku\\\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\\\/\\\/hcp.biomarin.com\\\/es-la\\\/pku\\\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Opciones de manejo de PKU\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\\\/\\\/hcp.biomarin.com\\\/es-la\\\/pku\\\/#website\",\"url\":\"https:\\\/\\\/hcp.biomarin.com\\\/es-la\\\/pku\\\/\",\"name\":\"BioMarin PKU DSE HCP ES-LA\",\"description\":\"\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\\\/\\\/hcp.biomarin.com\\\/es-la\\\/pku\\\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"es\"}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Opciones de tratamiento y terapia diet\u00e9tica de fenilcetonuria (PKU)","description":"En combinaci\u00f3n con una dieta con restricci\u00f3n de fenilalanina (Phe), existen otras opciones que pueden ayudar a reducir los niveles de Phe en sangre de pacientes con PKU.","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/hcp.biomarin.com\/es-la\/pku\/opciones-de-tratamiento-de-la-pku\/","og_locale":"es_ES","og_type":"article","og_title":"Opciones de tratamiento y terapia diet\u00e9tica de fenilcetonuria (PKU)","og_description":"En combinaci\u00f3n con una dieta con restricci\u00f3n de fenilalanina (Phe), existen otras opciones que pueden ayudar a reducir los niveles de Phe en sangre de pacientes con PKU.","og_url":"https:\/\/hcp.biomarin.com\/es-la\/pku\/opciones-de-tratamiento-de-la-pku\/","og_site_name":"BioMarin PKU DSE HCP ES-LA","article_modified_time":"2024-09-16T13:00:05+00:00","twitter_card":"summary_large_image","schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"WebPage","@id":"https:\/\/hcp.biomarin.com\/es-la\/pku\/opciones-de-tratamiento-de-la-pku\/","url":"https:\/\/hcp.biomarin.com\/es-la\/pku\/opciones-de-tratamiento-de-la-pku\/","name":"Opciones de tratamiento y terapia diet\u00e9tica de fenilcetonuria (PKU)","isPartOf":{"@id":"https:\/\/hcp.biomarin.com\/es-la\/pku\/#website"},"datePublished":"2023-01-12T06:03:14+00:00","dateModified":"2024-09-16T13:00:05+00:00","description":"En combinaci\u00f3n con una dieta con restricci\u00f3n de fenilalanina (Phe), existen otras opciones que pueden ayudar a reducir los niveles de Phe en sangre de pacientes con PKU.","breadcrumb":{"@id":"https:\/\/hcp.biomarin.com\/es-la\/pku\/opciones-de-tratamiento-de-la-pku\/#breadcrumb"},"inLanguage":"es","potentialAction":[{"@type":"ReadAction","target":["https:\/\/hcp.biomarin.com\/es-la\/pku\/opciones-de-tratamiento-de-la-pku\/"]}]},{"@type":"BreadcrumbList","@id":"https:\/\/hcp.biomarin.com\/es-la\/pku\/opciones-de-tratamiento-de-la-pku\/#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"Home","item":"https:\/\/hcp.biomarin.com\/es-la\/pku\/"},{"@type":"ListItem","position":2,"name":"Opciones de manejo de PKU"}]},{"@type":"WebSite","@id":"https:\/\/hcp.biomarin.com\/es-la\/pku\/#website","url":"https:\/\/hcp.biomarin.com\/es-la\/pku\/","name":"BioMarin PKU DSE HCP ES-LA","description":"","potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/hcp.biomarin.com\/es-la\/pku\/?s={search_term_string}"},"query-input":{"@type":"PropertyValueSpecification","valueRequired":true,"valueName":"search_term_string"}}],"inLanguage":"es"}]}},"_links":{"self":[{"href":"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-json\/wp\/v2\/pages\/764","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-json\/wp\/v2\/users\/3"}],"replies":[{"embeddable":true,"href":"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-json\/wp\/v2\/comments?post=764"}],"version-history":[{"count":165,"href":"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-json\/wp\/v2\/pages\/764\/revisions"}],"predecessor-version":[{"id":4682,"href":"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-json\/wp\/v2\/pages\/764\/revisions\/4682"}],"wp:attachment":[{"href":"https:\/\/hcp.biomarin.com\/es-la\/pku\/wp-json\/wp\/v2\/media?parent=764"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}