{"id":1829,"date":"2022-08-11T11:34:28","date_gmt":"2022-08-11T11:34:28","guid":{"rendered":"https:\/\/palynziqhcp-dev-001.azurewebsites.net\/en-us\/palynziq\/?page_id=1829"},"modified":"2024-06-12T14:06:36","modified_gmt":"2024-06-12T14:06:36","slug":"side-effects-and-safety-profile","status":"publish","type":"page","link":"https:\/\/hcp.biomarin.com\/en-us\/palynziq\/side-effects-and-safety-profile\/","title":{"rendered":"Safety Profile"},"content":{"rendered":"
As with all therapeutic proteins, there is potential for immunogenicity1<\/sup><\/p>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/figure>\n <\/div>\n <\/div>\n<\/div>\n\n\n \n \n \n\n Non\u2013IgE-mediated anaphylaxis was observed in PALYNZIQ clinical trials1,a<\/sup><\/h3>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/figure>\n <\/div>\n <\/div>\n<\/div>\n\n\n \n \n \n\n Anaphylaxis has been reported after administration of PALYNZIQ and may occur at any time during treatment1<\/sup><\/h3>\n\nMost episodes occurred within 1 hour after injection (81%; 34 of 42 episodes), though delayed episodes also occurred up to 48 hours after administration of PALYNZIQ1<\/sup><\/li>\nMost episodes occurred within 1 year of dosing (69%; 29 of 42 episodes), but cases also occurred after 1 year of dosing and up to 1604 days (4.4 years) of total follow-up1<\/sup><\/li>\n48% of anaphylaxis episodes (20 of 42 episodes) were managed with administration of auto-injectable epinephrine1<\/sup><\/li>\nConsider having an adult observer for patients who may need assistance in recognizing and managing anaphylaxis1<\/sup><\/li>\n<\/ul>\na <\/sup>27 of 29 patients who had anaphylaxis were tested for anti\u2013pegvaliase-pqpz IgE antibodies, which recognize the PEGylated protein product. Of those 27 patients, 26 tested negative. The one patient who screened positive for anti\u2013pegvaliase-pqpz IgE had insufficient sample to confirm IgE positivity. This patient tested negative for anti\u2013pegvaliase-pqpz IgE at routine visits before and after the anaphylaxis episode.1<\/sup><\/small><\/p>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n\t\n\t\t\n\t\t\t\n\t\t\t\t\n\t\t\t\t\t\n\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t\t Learn about different types of hypersensitivity\n<\/h2>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\n \n\n Type I vs Type III hypersensitivity<\/h2>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/figure>\n\t\t\t\t<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n \n \n\n In the clinical trials, the majority of adverse reactions were mild to moderate in severity1,2<\/sup><\/h3>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/figure>\n\n\n \n15% of patients (44 of 285) discontinued treatment due to an adverse event1<\/sup><\/li>\nThe most common adverse reactions leading to discontinuation were hypersensitivity reactions (6%), including anaphylaxis (3%), angioedema (1%), arthralgia (4%), generalized skin reactions lasting at least 14 days (2%), and ISRs (1%)1<\/sup><\/li>\n<\/ul>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n\t\n\t\t\n\t\t\t\n\t\t\t\t\n\t\t\t\t\t\n\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t\t View adverse reactions by exposure-adjusted rate\n<\/h2>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\n \n\n The exposure-adjusted rate of adverse reactions was highest during induction and titration, and generally decreased in the maintenance phase1<\/sup><\/h3>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/figure>\n\n\n c<\/sup>\u00a0Hypersensitivity, including anaphylaxis.<\/small><\/p>\n\nThe exposure-adjusted rate represents the number of episodes divided by person-years (the number of patients multiplied by the years patients were exposed to treatment)<\/small>\n\nIt is calculated by taking the number of events divided by the number of person-years (the number of patients multiplied by the number of years they were exposed to the treatment)<\/small><\/li>\n<\/ul>\n <\/div>\n\t\t\t\t<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n \n <\/div>\n <\/div>\n<\/div>\n\n\n \n \n \n\n Rates of the 3 most common adverse reactions decreased from induction\/titration to maintenance,d<\/sup> despite increasing dose1,6<\/sup><\/h3>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/p>\nc<\/sup>Hypersensitivity, including anaphylaxis.\nd<\/sup>Maintenance phase defined as when subjects reached stable dose for 8 weeks.\ne<\/sup>Hypersensitivity, including anaphylaxis.\nf<\/sup>Maintenance, all doses includes patients on placebo and PALYNZIQ doses <20 mg.<\/small><\/p>\n<\/figcaption>\n <\/figure>\n <\/div>\n <\/div>\n<\/div>\n\n\n \n\t\t\n\t\t\t\n\t\t\t\t<\/div>\n\t\t\t\t\n\t\t\t\t \t\t\t\t\t\n \n\t\t\t\t\t \t\t\t\t\t \t\t\t\t\t\t \t\t\t\t\t\t The types and rate of adverse reactions reported during the maintenance phase were similar in patients who received 20 mg, 40 mg, and 60 mg once daily.1<\/sup><\/h4>\n\t\t\t\t\t\t \t\t\t\t\t <\/div>\n\t\t\t\t\t <\/div>\n\t\t\t\t<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n \n \n\n \nThe exposure-adjusted rate of anaphylaxis was highest during induction and titration phases (0.25 episodes\/person-years) and decreased in the maintenance phase (0.05 episodes\/person-years)<\/li>\nThe frequency of hypersensitivity reactions with PALYNZIQ is highest early in treatment when the immune response is most reactive, but may occur at any time during treatment1<\/sup><\/li>\nLater in treatment, the immune response stabilizes1,3<\/sup><\/li>\nThe exposure-adjusted rate represents the number of episodes divided by person-years (the number of patients multiplied by the years patients were exposed to treatment)\n\nIt is calculated by taking the number of events divided by the number of person-years (the number of patients multiplied by the number of years they were exposed to the treatment)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n \n \n \n\n In clinical trials, adverse reactions were managed with medication, dose reduction, interruption, and discontinuation1<\/sup><\/h2>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n\t\n\t\t\n\t\t\t\n\t\t\t\t\t\t\t\t\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Premedication1<\/sup>\n<\/h3>\n Premedication may be considered, based on individual patient tolerability, prior to each dose of PALYNZIQ. Most frequently administered H1- and H2-receptor antagonists and antipyretics during PRISM-2 g,h,i,j<\/sup><\/p>\n\nranitidine hydrochloridej<\/sup><\/li>\nibuprofen<\/li>\nfexofenadine hydrochloride<\/li>\ncetirizine hydrochloride<\/li>\ndiphenhydramine hydrochloride<\/li>\nloratadine<\/li>\nacetaminophen<\/li>\nnaproxen sodium<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Anaphylaxis1<\/sup><\/span>\n<\/h3>\n \nMedication<\/strong>: managed with autoinjectable epinephrine, corticosteroids, antihistamines, and\/or oxygen<\/li>\nDose reduction<\/strong>: 9.5%<\/li>\nInterruption<\/strong>: 35.7% of patients<\/li>\nDiscontinuation<\/strong>: 21.4% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Arthralgia1<\/sup>\n<\/h3>\n \nMedication<\/strong>: managed with nonsteroidal anti-inflammatory drugs, glucocorticoids, and acetaminophen<\/li>\nDose reduction<\/strong>: 3.8% of patients<\/li>\nInterruption<\/strong>: 3.6% of patients<\/li>\nDiscontinuation<\/strong>: 0.6% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Injection site reactions1<\/sup>\n<\/h3>\n \nMedication<\/strong>: treated with topical antihistamine, corticosteroids<\/li>\nDose reduction<\/strong>: 0.4% of patients<\/li>\nInterruption<\/strong>: 0.3% of patients<\/li>\nDiscontinuation<\/strong>: 0.1% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n g<\/sup>Patients (n=215) may have been prescribed premedications in combination, and\/or may have switched between different premedication regimens during the study period.\n<\/small>h<\/sup>The rates of use of these medications in this population only partially reflects their use as premedications; these medications may also have been used to treat other conditions, such as seasonal allergies, headaches, etc.\n<\/small>i<\/sup>During PRISM-2, premedication was administered 2-3 hours prior to PALYNZIQ.\n<\/small>j<\/sup>Please note: the FDA has advised a voluntary recall of ranitidine made by many manufacturers, due to concerns over purity. Consider substituting a different H2 blocker.<\/small><\/p>\n <\/div>\n<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n\t\t\n\t\t \t\t\t References:\n<\/h4>\n\t\t\t\t\t\t \n PALYNZIQ [package insert]. Novato, CA: BioMarin Pharmaceutical Inc; 2020. \n<\/span><\/li>\n Thomas J, Levy H, Amato S, et al<\/em>, for the PRISM investigators. Pegvaliase for the treatment of phenylketonuria: results of a long-term phase 3 clinical trial program (PRISM). Mol Genet Metab<\/em>. 2018;124(1):27-38. \n<\/span><\/li>\n Gupta S, Lau K, Harding CO, et al<\/em>. Association of immune response with efficacy and safety outcomes in adults with phenylketonuria administered pegvaliase in phase 3 clinical trials. EBioMedicine<\/em>. 2018;37:366-373. \n<\/span><\/li>\n Monta\u00f1ez MI, Mayorga C, Bogas G, et al<\/em>. Epidemiology, mechanisms, and diagnosis of drug-induced anaphylaxis. Front Immunol<\/em>. 2017;8:1-10. \n<\/span><\/li>\n Hausmann O, Daha M, Longo N, et al<\/em>. Pegvaliase: immunological profile and recommendations for the clinical management of hypersensitivity reactions in patients with phenylketonuria treated with this enzyme substitution therapy. Mol Genet Metab<\/em>. 2019;128(1-2):84-91. doi:10.1016\/j.ymgme.2019.05.006. \n<\/span><\/li>\n
a <\/sup>27 of 29 patients who had anaphylaxis were tested for anti\u2013pegvaliase-pqpz IgE antibodies, which recognize the PEGylated protein product. Of those 27 patients, 26 tested negative. The one patient who screened positive for anti\u2013pegvaliase-pqpz IgE had insufficient sample to confirm IgE positivity. This patient tested negative for anti\u2013pegvaliase-pqpz IgE at routine visits before and after the anaphylaxis episode.1<\/sup><\/small><\/p>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n\t\n\t\t\n\t\t\t\n\t\t\t\t\n\t\t\t\t\t\n\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t\t Learn about different types of hypersensitivity\n<\/h2>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\n \n\n Type I vs Type III hypersensitivity<\/h2>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/figure>\n\t\t\t\t<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n \n \n\n In the clinical trials, the majority of adverse reactions were mild to moderate in severity1,2<\/sup><\/h3>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/figure>\n\n\n \n15% of patients (44 of 285) discontinued treatment due to an adverse event1<\/sup><\/li>\nThe most common adverse reactions leading to discontinuation were hypersensitivity reactions (6%), including anaphylaxis (3%), angioedema (1%), arthralgia (4%), generalized skin reactions lasting at least 14 days (2%), and ISRs (1%)1<\/sup><\/li>\n<\/ul>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n\t\n\t\t\n\t\t\t\n\t\t\t\t\n\t\t\t\t\t\n\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t\t\t View adverse reactions by exposure-adjusted rate\n<\/h2>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\n \n\n The exposure-adjusted rate of adverse reactions was highest during induction and titration, and generally decreased in the maintenance phase1<\/sup><\/h3>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/figure>\n\n\n c<\/sup>\u00a0Hypersensitivity, including anaphylaxis.<\/small><\/p>\n\nThe exposure-adjusted rate represents the number of episodes divided by person-years (the number of patients multiplied by the years patients were exposed to treatment)<\/small>\n\nIt is calculated by taking the number of events divided by the number of person-years (the number of patients multiplied by the number of years they were exposed to the treatment)<\/small><\/li>\n<\/ul>\n <\/div>\n\t\t\t\t<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n \n <\/div>\n <\/div>\n<\/div>\n\n\n \n \n \n\n Rates of the 3 most common adverse reactions decreased from induction\/titration to maintenance,d<\/sup> despite increasing dose1,6<\/sup><\/h3>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/p>\nc<\/sup>Hypersensitivity, including anaphylaxis.\nd<\/sup>Maintenance phase defined as when subjects reached stable dose for 8 weeks.\ne<\/sup>Hypersensitivity, including anaphylaxis.\nf<\/sup>Maintenance, all doses includes patients on placebo and PALYNZIQ doses <20 mg.<\/small><\/p>\n<\/figcaption>\n <\/figure>\n <\/div>\n <\/div>\n<\/div>\n\n\n \n\t\t\n\t\t\t\n\t\t\t\t<\/div>\n\t\t\t\t\n\t\t\t\t \t\t\t\t\t\n \n\t\t\t\t\t \t\t\t\t\t \t\t\t\t\t\t \t\t\t\t\t\t The types and rate of adverse reactions reported during the maintenance phase were similar in patients who received 20 mg, 40 mg, and 60 mg once daily.1<\/sup><\/h4>\n\t\t\t\t\t\t \t\t\t\t\t <\/div>\n\t\t\t\t\t <\/div>\n\t\t\t\t<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n \n \n\n \nThe exposure-adjusted rate of anaphylaxis was highest during induction and titration phases (0.25 episodes\/person-years) and decreased in the maintenance phase (0.05 episodes\/person-years)<\/li>\nThe frequency of hypersensitivity reactions with PALYNZIQ is highest early in treatment when the immune response is most reactive, but may occur at any time during treatment1<\/sup><\/li>\nLater in treatment, the immune response stabilizes1,3<\/sup><\/li>\nThe exposure-adjusted rate represents the number of episodes divided by person-years (the number of patients multiplied by the years patients were exposed to treatment)\n\nIt is calculated by taking the number of events divided by the number of person-years (the number of patients multiplied by the number of years they were exposed to the treatment)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n \n \n \n\n In clinical trials, adverse reactions were managed with medication, dose reduction, interruption, and discontinuation1<\/sup><\/h2>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n\t\n\t\t\n\t\t\t\n\t\t\t\t\t\t\t\t\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Premedication1<\/sup>\n<\/h3>\n Premedication may be considered, based on individual patient tolerability, prior to each dose of PALYNZIQ. Most frequently administered H1- and H2-receptor antagonists and antipyretics during PRISM-2 g,h,i,j<\/sup><\/p>\n\nranitidine hydrochloridej<\/sup><\/li>\nibuprofen<\/li>\nfexofenadine hydrochloride<\/li>\ncetirizine hydrochloride<\/li>\ndiphenhydramine hydrochloride<\/li>\nloratadine<\/li>\nacetaminophen<\/li>\nnaproxen sodium<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Anaphylaxis1<\/sup><\/span>\n<\/h3>\n \nMedication<\/strong>: managed with autoinjectable epinephrine, corticosteroids, antihistamines, and\/or oxygen<\/li>\nDose reduction<\/strong>: 9.5%<\/li>\nInterruption<\/strong>: 35.7% of patients<\/li>\nDiscontinuation<\/strong>: 21.4% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Arthralgia1<\/sup>\n<\/h3>\n \nMedication<\/strong>: managed with nonsteroidal anti-inflammatory drugs, glucocorticoids, and acetaminophen<\/li>\nDose reduction<\/strong>: 3.8% of patients<\/li>\nInterruption<\/strong>: 3.6% of patients<\/li>\nDiscontinuation<\/strong>: 0.6% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Injection site reactions1<\/sup>\n<\/h3>\n \nMedication<\/strong>: treated with topical antihistamine, corticosteroids<\/li>\nDose reduction<\/strong>: 0.4% of patients<\/li>\nInterruption<\/strong>: 0.3% of patients<\/li>\nDiscontinuation<\/strong>: 0.1% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n g<\/sup>Patients (n=215) may have been prescribed premedications in combination, and\/or may have switched between different premedication regimens during the study period.\n<\/small>h<\/sup>The rates of use of these medications in this population only partially reflects their use as premedications; these medications may also have been used to treat other conditions, such as seasonal allergies, headaches, etc.\n<\/small>i<\/sup>During PRISM-2, premedication was administered 2-3 hours prior to PALYNZIQ.\n<\/small>j<\/sup>Please note: the FDA has advised a voluntary recall of ranitidine made by many manufacturers, due to concerns over purity. Consider substituting a different H2 blocker.<\/small><\/p>\n <\/div>\n<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n\t\t\n\t\t \t\t\t References:\n<\/h4>\n\t\t\t\t\t\t \n PALYNZIQ [package insert]. Novato, CA: BioMarin Pharmaceutical Inc; 2020. \n<\/span><\/li>\n Thomas J, Levy H, Amato S, et al<\/em>, for the PRISM investigators. Pegvaliase for the treatment of phenylketonuria: results of a long-term phase 3 clinical trial program (PRISM). Mol Genet Metab<\/em>. 2018;124(1):27-38. \n<\/span><\/li>\n Gupta S, Lau K, Harding CO, et al<\/em>. Association of immune response with efficacy and safety outcomes in adults with phenylketonuria administered pegvaliase in phase 3 clinical trials. EBioMedicine<\/em>. 2018;37:366-373. \n<\/span><\/li>\n Monta\u00f1ez MI, Mayorga C, Bogas G, et al<\/em>. Epidemiology, mechanisms, and diagnosis of drug-induced anaphylaxis. Front Immunol<\/em>. 2017;8:1-10. \n<\/span><\/li>\n Hausmann O, Daha M, Longo N, et al<\/em>. Pegvaliase: immunological profile and recommendations for the clinical management of hypersensitivity reactions in patients with phenylketonuria treated with this enzyme substitution therapy. Mol Genet Metab<\/em>. 2019;128(1-2):84-91. doi:10.1016\/j.ymgme.2019.05.006. \n<\/span><\/li>\n
c<\/sup>\u00a0Hypersensitivity, including anaphylaxis.<\/small><\/p>\n\nThe exposure-adjusted rate represents the number of episodes divided by person-years (the number of patients multiplied by the years patients were exposed to treatment)<\/small>\n\nIt is calculated by taking the number of events divided by the number of person-years (the number of patients multiplied by the number of years they were exposed to the treatment)<\/small><\/li>\n<\/ul>\n <\/div>\n\t\t\t\t<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n \n <\/div>\n <\/div>\n<\/div>\n\n\n \n \n \n\n Rates of the 3 most common adverse reactions decreased from induction\/titration to maintenance,d<\/sup> despite increasing dose1,6<\/sup><\/h3>\n <\/div>\n\n\n \n \n\t\t\t \t\t\t<\/div>\n\t\t\t\n\t\t\t \t\t\t<\/div>\n <\/div>\n <\/p>\nc<\/sup>Hypersensitivity, including anaphylaxis.\nd<\/sup>Maintenance phase defined as when subjects reached stable dose for 8 weeks.\ne<\/sup>Hypersensitivity, including anaphylaxis.\nf<\/sup>Maintenance, all doses includes patients on placebo and PALYNZIQ doses <20 mg.<\/small><\/p>\n<\/figcaption>\n <\/figure>\n <\/div>\n <\/div>\n<\/div>\n\n\n \n\t\t\n\t\t\t\n\t\t\t\t<\/div>\n\t\t\t\t\n\t\t\t\t \t\t\t\t\t\n \n\t\t\t\t\t \t\t\t\t\t \t\t\t\t\t\t \t\t\t\t\t\t The types and rate of adverse reactions reported during the maintenance phase were similar in patients who received 20 mg, 40 mg, and 60 mg once daily.1<\/sup><\/h4>\n\t\t\t\t\t\t \t\t\t\t\t <\/div>\n\t\t\t\t\t <\/div>\n\t\t\t\t<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n \n \n\n \nThe exposure-adjusted rate of anaphylaxis was highest during induction and titration phases (0.25 episodes\/person-years) and decreased in the maintenance phase (0.05 episodes\/person-years)<\/li>\nThe frequency of hypersensitivity reactions with PALYNZIQ is highest early in treatment when the immune response is most reactive, but may occur at any time during treatment1<\/sup><\/li>\nLater in treatment, the immune response stabilizes1,3<\/sup><\/li>\nThe exposure-adjusted rate represents the number of episodes divided by person-years (the number of patients multiplied by the years patients were exposed to treatment)\n\nIt is calculated by taking the number of events divided by the number of person-years (the number of patients multiplied by the number of years they were exposed to the treatment)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n \n \n \n\n In clinical trials, adverse reactions were managed with medication, dose reduction, interruption, and discontinuation1<\/sup><\/h2>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n\t\n\t\t\n\t\t\t\n\t\t\t\t\t\t\t\t\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Premedication1<\/sup>\n<\/h3>\n Premedication may be considered, based on individual patient tolerability, prior to each dose of PALYNZIQ. Most frequently administered H1- and H2-receptor antagonists and antipyretics during PRISM-2 g,h,i,j<\/sup><\/p>\n\nranitidine hydrochloridej<\/sup><\/li>\nibuprofen<\/li>\nfexofenadine hydrochloride<\/li>\ncetirizine hydrochloride<\/li>\ndiphenhydramine hydrochloride<\/li>\nloratadine<\/li>\nacetaminophen<\/li>\nnaproxen sodium<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Anaphylaxis1<\/sup><\/span>\n<\/h3>\n \nMedication<\/strong>: managed with autoinjectable epinephrine, corticosteroids, antihistamines, and\/or oxygen<\/li>\nDose reduction<\/strong>: 9.5%<\/li>\nInterruption<\/strong>: 35.7% of patients<\/li>\nDiscontinuation<\/strong>: 21.4% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Arthralgia1<\/sup>\n<\/h3>\n \nMedication<\/strong>: managed with nonsteroidal anti-inflammatory drugs, glucocorticoids, and acetaminophen<\/li>\nDose reduction<\/strong>: 3.8% of patients<\/li>\nInterruption<\/strong>: 3.6% of patients<\/li>\nDiscontinuation<\/strong>: 0.6% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Injection site reactions1<\/sup>\n<\/h3>\n \nMedication<\/strong>: treated with topical antihistamine, corticosteroids<\/li>\nDose reduction<\/strong>: 0.4% of patients<\/li>\nInterruption<\/strong>: 0.3% of patients<\/li>\nDiscontinuation<\/strong>: 0.1% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n g<\/sup>Patients (n=215) may have been prescribed premedications in combination, and\/or may have switched between different premedication regimens during the study period.\n<\/small>h<\/sup>The rates of use of these medications in this population only partially reflects their use as premedications; these medications may also have been used to treat other conditions, such as seasonal allergies, headaches, etc.\n<\/small>i<\/sup>During PRISM-2, premedication was administered 2-3 hours prior to PALYNZIQ.\n<\/small>j<\/sup>Please note: the FDA has advised a voluntary recall of ranitidine made by many manufacturers, due to concerns over purity. Consider substituting a different H2 blocker.<\/small><\/p>\n <\/div>\n<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n\t\t\n\t\t \t\t\t References:\n<\/h4>\n\t\t\t\t\t\t \n PALYNZIQ [package insert]. Novato, CA: BioMarin Pharmaceutical Inc; 2020. \n<\/span><\/li>\n Thomas J, Levy H, Amato S, et al<\/em>, for the PRISM investigators. Pegvaliase for the treatment of phenylketonuria: results of a long-term phase 3 clinical trial program (PRISM). Mol Genet Metab<\/em>. 2018;124(1):27-38. \n<\/span><\/li>\n Gupta S, Lau K, Harding CO, et al<\/em>. Association of immune response with efficacy and safety outcomes in adults with phenylketonuria administered pegvaliase in phase 3 clinical trials. EBioMedicine<\/em>. 2018;37:366-373. \n<\/span><\/li>\n Monta\u00f1ez MI, Mayorga C, Bogas G, et al<\/em>. Epidemiology, mechanisms, and diagnosis of drug-induced anaphylaxis. Front Immunol<\/em>. 2017;8:1-10. \n<\/span><\/li>\n Hausmann O, Daha M, Longo N, et al<\/em>. Pegvaliase: immunological profile and recommendations for the clinical management of hypersensitivity reactions in patients with phenylketonuria treated with this enzyme substitution therapy. Mol Genet Metab<\/em>. 2019;128(1-2):84-91. doi:10.1016\/j.ymgme.2019.05.006. \n<\/span><\/li>\n
<\/p>\n
c<\/sup>Hypersensitivity, including anaphylaxis.\nd<\/sup>Maintenance phase defined as when subjects reached stable dose for 8 weeks.\ne<\/sup>Hypersensitivity, including anaphylaxis.\nf<\/sup>Maintenance, all doses includes patients on placebo and PALYNZIQ doses <20 mg.<\/small><\/p>\n<\/figcaption>\n <\/figure>\n <\/div>\n <\/div>\n<\/div>\n\n\n \n\t\t\n\t\t\t\n\t\t\t\t<\/div>\n\t\t\t\t\n\t\t\t\t \t\t\t\t\t\n \n\t\t\t\t\t \t\t\t\t\t \t\t\t\t\t\t \t\t\t\t\t\t The types and rate of adverse reactions reported during the maintenance phase were similar in patients who received 20 mg, 40 mg, and 60 mg once daily.1<\/sup><\/h4>\n\t\t\t\t\t\t \t\t\t\t\t <\/div>\n\t\t\t\t\t <\/div>\n\t\t\t\t<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n \n \n\n \nThe exposure-adjusted rate of anaphylaxis was highest during induction and titration phases (0.25 episodes\/person-years) and decreased in the maintenance phase (0.05 episodes\/person-years)<\/li>\nThe frequency of hypersensitivity reactions with PALYNZIQ is highest early in treatment when the immune response is most reactive, but may occur at any time during treatment1<\/sup><\/li>\nLater in treatment, the immune response stabilizes1,3<\/sup><\/li>\nThe exposure-adjusted rate represents the number of episodes divided by person-years (the number of patients multiplied by the years patients were exposed to treatment)\n\nIt is calculated by taking the number of events divided by the number of person-years (the number of patients multiplied by the number of years they were exposed to the treatment)<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n \n \n \n\n In clinical trials, adverse reactions were managed with medication, dose reduction, interruption, and discontinuation1<\/sup><\/h2>\n <\/div>\n <\/div>\n <\/div>\n<\/div>\n\n\n\t\n\t\t\n\t\t\t\n\t\t\t\t\t\t\t\t\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Premedication1<\/sup>\n<\/h3>\n Premedication may be considered, based on individual patient tolerability, prior to each dose of PALYNZIQ. Most frequently administered H1- and H2-receptor antagonists and antipyretics during PRISM-2 g,h,i,j<\/sup><\/p>\n\nranitidine hydrochloridej<\/sup><\/li>\nibuprofen<\/li>\nfexofenadine hydrochloride<\/li>\ncetirizine hydrochloride<\/li>\ndiphenhydramine hydrochloride<\/li>\nloratadine<\/li>\nacetaminophen<\/li>\nnaproxen sodium<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Anaphylaxis1<\/sup><\/span>\n<\/h3>\n \nMedication<\/strong>: managed with autoinjectable epinephrine, corticosteroids, antihistamines, and\/or oxygen<\/li>\nDose reduction<\/strong>: 9.5%<\/li>\nInterruption<\/strong>: 35.7% of patients<\/li>\nDiscontinuation<\/strong>: 21.4% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Arthralgia1<\/sup>\n<\/h3>\n \nMedication<\/strong>: managed with nonsteroidal anti-inflammatory drugs, glucocorticoids, and acetaminophen<\/li>\nDose reduction<\/strong>: 3.8% of patients<\/li>\nInterruption<\/strong>: 3.6% of patients<\/li>\nDiscontinuation<\/strong>: 0.6% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Injection site reactions1<\/sup>\n<\/h3>\n \nMedication<\/strong>: treated with topical antihistamine, corticosteroids<\/li>\nDose reduction<\/strong>: 0.4% of patients<\/li>\nInterruption<\/strong>: 0.3% of patients<\/li>\nDiscontinuation<\/strong>: 0.1% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n g<\/sup>Patients (n=215) may have been prescribed premedications in combination, and\/or may have switched between different premedication regimens during the study period.\n<\/small>h<\/sup>The rates of use of these medications in this population only partially reflects their use as premedications; these medications may also have been used to treat other conditions, such as seasonal allergies, headaches, etc.\n<\/small>i<\/sup>During PRISM-2, premedication was administered 2-3 hours prior to PALYNZIQ.\n<\/small>j<\/sup>Please note: the FDA has advised a voluntary recall of ranitidine made by many manufacturers, due to concerns over purity. Consider substituting a different H2 blocker.<\/small><\/p>\n <\/div>\n<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n\t\t\n\t\t \t\t\t References:\n<\/h4>\n\t\t\t\t\t\t \n PALYNZIQ [package insert]. Novato, CA: BioMarin Pharmaceutical Inc; 2020. \n<\/span><\/li>\n Thomas J, Levy H, Amato S, et al<\/em>, for the PRISM investigators. Pegvaliase for the treatment of phenylketonuria: results of a long-term phase 3 clinical trial program (PRISM). Mol Genet Metab<\/em>. 2018;124(1):27-38. \n<\/span><\/li>\n Gupta S, Lau K, Harding CO, et al<\/em>. Association of immune response with efficacy and safety outcomes in adults with phenylketonuria administered pegvaliase in phase 3 clinical trials. EBioMedicine<\/em>. 2018;37:366-373. \n<\/span><\/li>\n Monta\u00f1ez MI, Mayorga C, Bogas G, et al<\/em>. Epidemiology, mechanisms, and diagnosis of drug-induced anaphylaxis. Front Immunol<\/em>. 2017;8:1-10. \n<\/span><\/li>\n Hausmann O, Daha M, Longo N, et al<\/em>. Pegvaliase: immunological profile and recommendations for the clinical management of hypersensitivity reactions in patients with phenylketonuria treated with this enzyme substitution therapy. Mol Genet Metab<\/em>. 2019;128(1-2):84-91. doi:10.1016\/j.ymgme.2019.05.006. \n<\/span><\/li>\n
Premedication may be considered, based on individual patient tolerability, prior to each dose of PALYNZIQ. Most frequently administered H1- and H2-receptor antagonists and antipyretics during PRISM-2 g,h,i,j<\/sup><\/p>\n\nranitidine hydrochloridej<\/sup><\/li>\nibuprofen<\/li>\nfexofenadine hydrochloride<\/li>\ncetirizine hydrochloride<\/li>\ndiphenhydramine hydrochloride<\/li>\nloratadine<\/li>\nacetaminophen<\/li>\nnaproxen sodium<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Anaphylaxis1<\/sup><\/span>\n<\/h3>\n \nMedication<\/strong>: managed with autoinjectable epinephrine, corticosteroids, antihistamines, and\/or oxygen<\/li>\nDose reduction<\/strong>: 9.5%<\/li>\nInterruption<\/strong>: 35.7% of patients<\/li>\nDiscontinuation<\/strong>: 21.4% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Arthralgia1<\/sup>\n<\/h3>\n \nMedication<\/strong>: managed with nonsteroidal anti-inflammatory drugs, glucocorticoids, and acetaminophen<\/li>\nDose reduction<\/strong>: 3.8% of patients<\/li>\nInterruption<\/strong>: 3.6% of patients<\/li>\nDiscontinuation<\/strong>: 0.6% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n \n \n <\/div>\n <\/figure>\n <\/div>\n \n Injection site reactions1<\/sup>\n<\/h3>\n \nMedication<\/strong>: treated with topical antihistamine, corticosteroids<\/li>\nDose reduction<\/strong>: 0.4% of patients<\/li>\nInterruption<\/strong>: 0.3% of patients<\/li>\nDiscontinuation<\/strong>: 0.1% of patients<\/li>\n<\/ul>\n <\/div>\n<\/div>\n\n\n \n g<\/sup>Patients (n=215) may have been prescribed premedications in combination, and\/or may have switched between different premedication regimens during the study period.\n<\/small>h<\/sup>The rates of use of these medications in this population only partially reflects their use as premedications; these medications may also have been used to treat other conditions, such as seasonal allergies, headaches, etc.\n<\/small>i<\/sup>During PRISM-2, premedication was administered 2-3 hours prior to PALYNZIQ.\n<\/small>j<\/sup>Please note: the FDA has advised a voluntary recall of ranitidine made by many manufacturers, due to concerns over purity. Consider substituting a different H2 blocker.<\/small><\/p>\n <\/div>\n<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n\t\t\n\t\t \t\t\t References:\n<\/h4>\n\t\t\t\t\t\t \n PALYNZIQ [package insert]. Novato, CA: BioMarin Pharmaceutical Inc; 2020. \n<\/span><\/li>\n Thomas J, Levy H, Amato S, et al<\/em>, for the PRISM investigators. Pegvaliase for the treatment of phenylketonuria: results of a long-term phase 3 clinical trial program (PRISM). Mol Genet Metab<\/em>. 2018;124(1):27-38. \n<\/span><\/li>\n Gupta S, Lau K, Harding CO, et al<\/em>. Association of immune response with efficacy and safety outcomes in adults with phenylketonuria administered pegvaliase in phase 3 clinical trials. EBioMedicine<\/em>. 2018;37:366-373. \n<\/span><\/li>\n Monta\u00f1ez MI, Mayorga C, Bogas G, et al<\/em>. Epidemiology, mechanisms, and diagnosis of drug-induced anaphylaxis. Front Immunol<\/em>. 2017;8:1-10. \n<\/span><\/li>\n Hausmann O, Daha M, Longo N, et al<\/em>. Pegvaliase: immunological profile and recommendations for the clinical management of hypersensitivity reactions in patients with phenylketonuria treated with this enzyme substitution therapy. Mol Genet Metab<\/em>. 2019;128(1-2):84-91. doi:10.1016\/j.ymgme.2019.05.006. \n<\/span><\/li>\n
g<\/sup>Patients (n=215) may have been prescribed premedications in combination, and\/or may have switched between different premedication regimens during the study period.\n<\/small>h<\/sup>The rates of use of these medications in this population only partially reflects their use as premedications; these medications may also have been used to treat other conditions, such as seasonal allergies, headaches, etc.\n<\/small>i<\/sup>During PRISM-2, premedication was administered 2-3 hours prior to PALYNZIQ.\n<\/small>j<\/sup>Please note: the FDA has advised a voluntary recall of ranitidine made by many manufacturers, due to concerns over purity. Consider substituting a different H2 blocker.<\/small><\/p>\n <\/div>\n<\/div>\n\t\t\t<\/div>\n\t\t<\/div>\n\t<\/div>\n<\/div>\n\n\n \n\t\t\n\t\t \t\t\t References:\n<\/h4>\n\t\t\t\t\t\t \n PALYNZIQ [package insert]. Novato, CA: BioMarin Pharmaceutical Inc; 2020. \n<\/span><\/li>\n Thomas J, Levy H, Amato S, et al<\/em>, for the PRISM investigators. Pegvaliase for the treatment of phenylketonuria: results of a long-term phase 3 clinical trial program (PRISM). Mol Genet Metab<\/em>. 2018;124(1):27-38. \n<\/span><\/li>\n Gupta S, Lau K, Harding CO, et al<\/em>. Association of immune response with efficacy and safety outcomes in adults with phenylketonuria administered pegvaliase in phase 3 clinical trials. EBioMedicine<\/em>. 2018;37:366-373. \n<\/span><\/li>\n Monta\u00f1ez MI, Mayorga C, Bogas G, et al<\/em>. Epidemiology, mechanisms, and diagnosis of drug-induced anaphylaxis. Front Immunol<\/em>. 2017;8:1-10. \n<\/span><\/li>\n Hausmann O, Daha M, Longo N, et al<\/em>. Pegvaliase: immunological profile and recommendations for the clinical management of hypersensitivity reactions in patients with phenylketonuria treated with this enzyme substitution therapy. Mol Genet Metab<\/em>. 2019;128(1-2):84-91. doi:10.1016\/j.ymgme.2019.05.006. \n<\/span><\/li>\n